Monday, 24 August 2020

Genetics of PCO

 PCOS is the most   common female   endocrine    disorder   affecting some  5-15% of all women   in their reproductive    years. It is   a notoriously   heterogeneous   syndrome which runs within families. It has  a high degree of heritability and   is currently  looked upon as being  a complex   genetic  disorder.

Several hundreds   of candidate   genes have been studied however the    majority of these  genetic   variants have not   been replicated in sufficiently  large case control studies . Genetic   variants   in the fibrillin  gene  , the Androgen  receptor, FTO  gene the insulin   receptor , the FSHR    gene, the  TNF    alpha gene    and some variants   in the lL-6   gene do confer  a certain  risk for   PCOS   and have been   replicated in sufficiently large studies or meta analyses.

More  recently, GWAS   has identified up to 20  genetic   variants genes  involved    in neuroendocrine, metabolic and reproductive pathways. These studies   also provided   evidence   for shared biologic  pathways between PCOS   and a  number   of metabolic   disorders menopause   depression  and   male- pattern balding and a putative  male phenotype.

 

There is   not much   of overlap between GWAS   findings and most functional    molecular studies. However   most of the   identified SNPs seem to paly  a role in a pathway  responsible for trafficking   and recycling   of large  protein  transmembrane    receptors.

 

Moreover   some promising  SNPs   involved   in  gonadotropin  action have been   identified  which do  not only constitute   risk factors    for PCOS   but also  seem  to influence  response to ovulation   induction  treatment.

Lastly    but not least evidence   is accumulating   that epigenetic   mechanisms  might   as well play a role in  the pathogenesis of PCOS   either    during   fetal  programming or in later life via factors as obesity  and diet composition .

In conclusion   genetic studies   have shown   that neuroendocrine, metabolic   and reproductive  pathways   are involved   in the  pathogenesis      of PCOS.  Genetic   findings     are strikingly   consistent    between different   PCOS   phenotypes. There is genetic      evidence    for shared biologic pathways    between  PCOS  and a  number   of metabolic disorders, menopause, depression  and   male- pattern   balding , the putative male  phenotype

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